Summary

Name MCCC1
Full Name Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
Synonyms MCCase subunit alpha, 3-methylcrotonyl-CoA carboxylase 1, 3-methylcrotonyl-CoA carboxylase biotin-containing subunit, 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha | MCCA
Primary ID Q96RQ3
Links - -
Type protein
Relations 1
Function Biotin-attachment subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism.

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Relations

Regulator Mechanism target score
+ form complex img/form-complex.png binding Methylcrotonyl-CoA carboxylase complex
Publications: 1 Organism: Homo Sapiens