Summary

Name MMUT
Full Name Methylmalonyl-CoA mutase, mitochondrial
Synonyms MCM, Methylmalonyl-CoA isomerase |
Primary ID P22033
Links - -
Type protein
Relations 2
Function Catalyzes the reversible isomerization of methylmalonyl-CoA (MMCoA) (generated from branched-chain amino acid metabolism and degradation of dietary odd chain fatty acids and cholesterol) to succinyl-CoA (3-carboxypropionyl-CoA), a key intermediate of the tricarboxylic acid cycle.

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Relations

Regulator Mechanism target score
+ down-regulates quantity img/direct_inhibition.png chemical modification (S)-methylmalonyl-CoA(5-) 0.8
Publications: 1 Organism: Homo Sapiens
+ up-regulates quantity img/direct-activation.png chemical modification succinyl-CoA(5-) 0.8
Publications: 1 Organism: Homo Sapiens