Summary

Name BBOX1
Full Name Gamma-butyrobetaine dioxygenase
Synonyms Gamma-butyrobetaine hydroxylase, Gamma-BBH, Gamma-butyrobetaine,2-oxoglutarate dioxygenase | BBH, BBOX
Primary ID O75936
Links - -
Type protein
Relations 4
Pathways Carnitine biosynthesis
Function Catalyzes the formation of L-carnitine from gamma-butyrobetaine.

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Relations

Regulator Mechanism target score
+ down-regulates quantity img/direct_inhibition.png chemical modification 2-oxoglutarate(2-) 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis
+ up-regulates quantity img/direct-activation.png chemical modification succinate(2-) 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis
+ up-regulates quantity img/direct-activation.png chemical modification carnitine 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis
+ down-regulates quantity img/direct_inhibition.png chemical modification 4-(trimethylammonio)butanoate 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis