Summary

Name BCKDHA
Full Name 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
Synonyms Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain, BCKDE1A, BCKDH E1-alpha
Primary ID P12694
Links - -
Type protein
Relations 2
Function The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components

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Modifications Tables

Relations

Regulator Mechanism target score
+ down-regulates img/direct_inhibition.png phosphorylation BCKDHA 0.592
Publications: 1 Organism: Homo Sapiens
Tissue: Skeletal Muscle, Brain, Heart, Kidney
+ up-regulates activity img/direct-activation.png dephosphorylation BCKDHA 0.777
Publications: 1 Organism: Mus Musculus