Summary

Name TMLHE
Full Name Trimethyllysine dioxygenase, mitochondrial
Synonyms Epsilon-trimethyllysine 2-oxoglutarate dioxygenase, Epsilon-trimethyllysine hydroxylase, TML hydroxylase, TML-alpha-ketoglutarate dioxygenase, TML dioxygenase, TMLD | TMLH
Primary ID Q9NVH6
Links - -
Type protein
Relations 4
Pathways Carnitine biosynthesis
Function Converts trimethyllysine (TML) into hydroxytrimethyllysine (HTML) (PubMed:11431483, PubMed:23092983).

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Relations

Regulator Mechanism target score
+ down-regulates quantity img/direct_inhibition.png chemical modification N(6),N(6),N(6)-trimethyl-L-lysine 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis
+ down-regulates quantity img/direct_inhibition.png chemical modification 2-oxoglutarate(2-) 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis
+ up-regulates quantity img/direct-activation.png chemical modification succinate(2-) 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis
+ up-regulates quantity img/direct-activation.png chemical modification 3-hydroxy-N(6),N(6),N(6)-trimethyl-L-lysine 0.8
Publications: 1 Organism: Homo Sapiens
Pathways:Carnitine biosynthesis